Caenorhabditis elegans as a model for lysosomal storage disorders
نویسندگان
چکیده
منابع مشابه
Treatments for lysosomal storage disorders.
There are over 70 human diseases that are caused by defects in various aspects of lysosomal function. Until 20 years ago, the only specific therapy available for lysosomal storage disorders was allogeneic haemopoietic stem cell transplantation. Over the last two decades, there has been remarkable progress and there are now licensed treatments for seven of these diseases. In some cases, a choice...
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ژورنال
عنوان ژورنال: Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease
سال: 2008
ISSN: 0925-4439
DOI: 10.1016/j.bbadis.2008.04.003